This book brings together contemporary experts in bladder exstrophy-epispadias from around the world to present evidence-based recommendations for managing this anomaly from prenatal diagnosis, postnatal management, surgical reconstruction, long-term management, sexual and fertility implications, and psychosocial impacts on the patient, family and immediate community ecosystem. Bladder exstrophy and epispadias is relatively rare in its incidence, but remains, perhaps, the most complex congenital anomaly faced by pediatric urologists. When presented with an infant with this anomaly, there remains great controversy in every aspect of management of this disorderfrom what causes it, to when it should be repaired, to how it should be repaired, and what long-term management should entail. Pediatric urologists are only now beginning to seriously explore new strategies in dealing with bladder exstrophy, and long-term studies are being initiated and completed presenting a clearer picture on how this anomalywith serious long-term consequencesshould be managed. Moreover, bladder exstrophy is a global problem and its incidence is greater in the developing world.
Bladder Exstrophy and Epispadias: A Compendium begins by covering diagnosis and imaging, followed by surgical considerations and expected outcomes of repair. From here, various surgical repair methods, like complete primary repair, modern staged repair, Kelly repair, and various alternative approaches are covered in detail. A video library offering step by step depictions of each of the surgical approaches for bladder exstrophy, epispadias and cloacal exstrophy repairs offers the reader a unique, invaluable resource. This book is unique in including a global perspective on how this condition should be addressed in the face of disparities in access to careespecially in the Global South. Finally, a discussion of long-term results and the gynecological implications of exstrophy leads into a view of the patient and family perspective.
This is an ideal guide for urologists, pediatric urologists, surgeons, and students to be able to successfully diagnose, treat, and manage bladder exstrophy and epispadias.
Epidemiology and Embryology of the Bladder Exstrophy Epispadias
Complex.- Bladder exstrophy epispadias complex (BEEC): Prenatal Diagnosis
and Counseling.- Bladder Exstrophy Genetics Our Current Understanding.-
Prenatal and Postnatal Imaging of the Epispadias-Exstrophy Complex.- Surgical
ConsiderationsIndications and Timing for Surgery (Defining Outcomes and
Expectations of Exstrophy Repair).- Complete Primary Repair of Bladder
Exstrophy.- The Modern Staged Repair of Classic Bladder Exstrophy.- The Kelly
procedure.- Scroto-Perineal Appraoch to Bladder Exstrophy Repair.- Surgical
Management of Male Classic Bladder Exstrophy the Toronto Approach.-
Modified Perineal Approach to Repair Female Epispadias.- Bladder Exstrophy
and Epispadias Complex: A Compendium.- Common Adjuvant Surgeries in
Exstrophy/ Epispadias Care.- Continent Anal Urinary Diversions in Bladder
Exstrophy.- Cloacal Exstrophy.- Male Epispadias.- The Failed Exstrophy
Repair: Technique and Implications.- Perioperative Management of Bladder
Exstrophy.- Exstrophy as a Global Health Concern: Strategies for Addressing
the Burden of Disease.- Incontinence in Exstrophy-Epispadias: Should we
change our thinking?.- Surgical Options for Refractory Urinary Incontinence
in Classic Bladder Exstrophy.- Urinary Reconstruction in the Developing
World--Special Consideration and Technique.- Kidney and Bladder
Exstrophy--Considerations and Caution.- Role of nursing in the early care of
patients with bladder exstrophy.- The Impact of Physical Therapy on the
Bladder Exstrophy-Epispadias Complex.- Psychological Implications of Bladder
Exstrophy-Epispadias.- Reproductive and Sexual Health in Bladder Exstrophy.-
Gynecological Implications of Exstrophy.- Advocacy for the Exstrophy Patient
and Community: Empowering and Encouraging the Patient and Family.
Aseem Ravindra Shukla, MD, MHCI, Endowed Chair and Director of Minimally Invasive Surgery, Childrens Hospital of Philadelphia, Professor of Surgery (Urology) Perelman School of Medicine, University of Pennsylvania
Rakesh S. Joshi, M. Ch., Head of Department, Paediatric Surgery, Superintendent/CEO, Civil Hospital, Ahmedabad, India
Joao Luiz Pippi Salle, MD, PhD, FAAP, FRCSC Professor of Urology, Division of Urology, Toronto Hospital for Sick Kids Inaugural Chair Women's Auxiliary Chair in Urology Toronto, Canada
Paul A. Merguerian MD MS
Professof of Urology
University of Washington
Seattle Childrens Hospital
Seattle, Washington, USA
Pramod Reddy, MD, The Curtis Sheldon and Jeffrey Wacksman Chair of Pediatric Urology, Janszen Endowed Scholar in Urology, Director, Division of Pediatric Urology, Cincinnati Childrens, Professor of Urology Univ of Cincinnati College of Medicine, Cincinnati, Ohio.
Jaishri Ramji, M.Ch Professor, Department of Pediatric Surgery, B.J.Medical College and Civil Hospital, Ahmedabad.
Dana A. Weiss, MD Howard M. Snyder III Endowed Chair in Pediatric Urology, Associate Professor of Urology (in Surgery), Children's Hospital of Philadelphia, Perelman School of Medicine at the University of Pennsylvania
