Contributors |
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7 | (2) |
Preface |
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9 | (1) |
Dedications |
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10 | (1) |
Abbreviations |
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11 | (6) |
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Chapter 1 Neurologic diagnosis |
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17 | (64) |
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17 | (1) |
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The diagnostic process in neurology |
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18 | (3) |
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21 | (21) |
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Lumbar puncture and CSF examination |
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42 | (3) |
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Neurophysiologic examination |
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45 | (21) |
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Imaging the brain and spine |
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66 | (15) |
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Chapter 2 Disorders of consciousness |
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81 | (30) |
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81 | (11) |
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92 | (1) |
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Persistent/permanent vegetative state |
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93 | (2) |
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Minimally conscious state |
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95 | (1) |
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95 | (1) |
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96 | (7) |
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Hypoxic--ischemic encephalopathy |
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103 | (4) |
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Central pontine myelinolysis |
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107 | (4) |
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111 | (24) |
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111 | (1) |
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111 | (1) |
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112 | (2) |
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114 | (1) |
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115 | (1) |
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116 | (1) |
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Investigation and diagnosis |
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116 | (7) |
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123 | (12) |
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135 | (20) |
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135 | (4) |
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139 | (10) |
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149 | (1) |
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150 | (5) |
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155 | (20) |
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155 | (14) |
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169 | (6) |
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Chapter 6 Hyperkinetic movement disorders |
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175 | (32) |
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175 | (1) |
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176 | (11) |
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187 | (3) |
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190 | (4) |
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194 | (5) |
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199 | (2) |
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201 | (1) |
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202 | (1) |
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Drug-induced movement disorders |
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203 | (2) |
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Psychogenic movement disorders |
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205 | (2) |
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Chapter 7 Developmental diseases of the nervous system |
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207 | (46) |
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207 | (1) |
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Embryonic development of the nervous system |
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207 | (2) |
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Developmental malformations of the nervous system |
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209 | (18) |
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Defects in neural tube formation |
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210 | (5) |
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Defects in hindbrain development |
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215 | (5) |
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Defects in forebrain and cerebral development |
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220 | (7) |
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227 | (26) |
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228 | (6) |
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234 | (3) |
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237 | (4) |
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241 | (2) |
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Hereditary hemorrhagic telangiectasia (Osler--Rendu--Weber syndrome) |
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243 | (3) |
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Linear nevus sebaceous syndrome |
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246 | (1) |
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Cowden's syndrome and Lhermitte--Duclos disease |
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247 | (1) |
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Von Hippel--Lindau disease |
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248 | (1) |
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248 | (2) |
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250 | (3) |
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Chapter 8 Hereditary and metabolic diseases of the central nervous system in adults |
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253 | (26) |
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253 | (2) |
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Metabolic and degenerative diseases in adults |
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255 | (7) |
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255 | (2) |
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Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy |
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257 | (1) |
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Fragile X-associated tremor/ataxia syndrome |
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258 | (1) |
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X-linked adrenoleukodystrophy |
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259 | (2) |
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Pantothenate kinase-associated neurodegeneration |
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261 | (1) |
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Inherited diseases with prominent visceral and neurologic findings |
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262 | (3) |
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262 | (2) |
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Acute intermittent porphyria |
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264 | (1) |
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Disorders of amino acid metabolism |
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265 | (4) |
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265 | (4) |
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269 | (2) |
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269 | (1) |
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Adult neuronal ceroid lipofuscinoses |
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270 | (1) |
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Late-onset lysosomal storage diseases |
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271 | (4) |
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Late-onset GM2 gangliosidosis |
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271 | (1) |
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Late-onset metachromatic leukodystrophy |
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272 | (1) |
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273 | (1) |
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Late-onset Krabbe disease |
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274 | (1) |
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274 | (1) |
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275 | (4) |
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Diseases of mitochondrial DNA |
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276 | (3) |
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Chapter 9 Trauma of the brain and spinal cord |
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|
279 | (12) |
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Prasad S.S. V. Vannemreddy |
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279 | (1) |
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279 | (4) |
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283 | (1) |
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284 | (7) |
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Chapter 10 Stroke and transient ischemic attacks of the brain and eye |
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291 | (130) |
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291 | (3) |
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294 | (2) |
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296 | (25) |
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321 | (2) |
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323 | (20) |
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343 | (26) |
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369 | (7) |
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376 | (5) |
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381 | (40) |
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Chapter 11 Infections of the central nervous system |
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421 | (60) |
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Acute bacterial meningitis |
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421 | (5) |
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426 | (3) |
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429 | (4) |
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433 | (2) |
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435 | (4) |
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439 | (2) |
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441 | (3) |
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444 | (3) |
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447 | (5) |
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452 | (2) |
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454 | (3) |
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Progressive multifocal leukoencephalopathy (PML) |
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457 | (3) |
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460 | (3) |
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463 | (2) |
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465 | (3) |
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468 | (2) |
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470 | (2) |
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Creutzfeldt-Jakob disease (CJD) |
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472 | (9) |
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Chapter 12 Inflammatory disorders of the nervous system |
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481 | (26) |
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Acute disseminated encephalomyelitis (post-infectious encephalomyelitis) |
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481 | (3) |
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484 | (13) |
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497 | (5) |
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502 | (5) |
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Chapter 13 Tumors of the nervous system |
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|
507 | (38) |
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507 | (8) |
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515 | (7) |
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522 | (4) |
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526 | (1) |
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|
527 | (2) |
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Vestibular schwannoma (acoustic neuroma) |
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529 | (1) |
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Primary central nervous system lymphoma |
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|
530 | (2) |
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Germ cell tumors of the CNS |
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532 | (1) |
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Von Hippel--Lindau disease |
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|
533 | (3) |
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|
536 | (3) |
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Paraneoplastic neurologic disease |
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|
539 | (6) |
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Chapter 14 Degenerative diseases of the nervous system |
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|
545 | (96) |
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|
545 | (32) |
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|
545 | (10) |
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Frontotemporal dementia (FID) |
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|
555 | (5) |
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Dementia with Lewy bodies (DLB) |
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|
560 | (4) |
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564 | (4) |
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568 | (7) |
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Normal pressure hydrocephalus |
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|
575 | (2) |
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Parkinson's disease and parkinsonian disorders |
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|
577 | (35) |
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|
577 | (1) |
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Primary (idiopathic) parkinsonism: Parkinson's disease |
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|
578 | (18) |
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Multisystem degenerations (`Parkinsonism plus' or atypical parkinsonism) |
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|
596 | (12) |
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Heredodegenerative and secondary parkinsonism |
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|
608 | (4) |
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612 | (29) |
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|
612 | (1) |
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|
612 | (4) |
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Autosomal dominant cerebellar ataxias |
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616 | (9) |
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Autosomal recessive cerebellar ataxias |
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625 | (8) |
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X-linked causes of ataxia |
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|
633 | (8) |
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Chapter 15 Acquired metabolic diseases of the nervous system |
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641 | (26) |
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Thiamine deficiency: Wernicke--Korsakoff syndrome |
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641 | (4) |
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645 | (5) |
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|
650 | (3) |
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Niacin (nicotinic acid) deficiency |
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|
653 | (1) |
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Marchiafava--Bignami disease |
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|
654 | (1) |
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|
655 | (6) |
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|
661 | (1) |
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Posterior reversible encephalopathy syndrome |
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|
662 | (5) |
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Chapter 16 Disorders of circulation of the cerebrospinal fluid |
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667 | (12) |
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|
667 | (1) |
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Aqueductal stenosis with hydrocephalus |
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|
668 | (2) |
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Communicating hydrocepahalus |
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|
670 | (1) |
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Normal pressure hydrocephalus |
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|
671 | (1) |
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|
672 | (2) |
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Syringomyelia (syringohydromyelia) |
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|
674 | (1) |
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Idiopathic intracranial hypertension (pseudotumor cerebri) |
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|
675 | (2) |
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Intracranial hypotension syndrome |
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|
677 | (2) |
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Chapter 17 Cranial neuropathies I, V, and VII--XII |
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|
679 | (30) |
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Olfactory nerve neuropathy (cranial nerve I) |
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|
679 | (3) |
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Trigeminal nerve neuropathy (cranial nerve V) |
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|
682 | (5) |
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Selected conditions affecting the trigeminal nerve |
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|
687 | (3) |
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Facial nerve neuropathy (cranial nerve VII) |
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|
690 | (4) |
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Selected conditions affecting the facial nerve |
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|
694 | (2) |
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Vestibulo-cochlear nerve neuropathy (cranial nerve VIII) |
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|
696 | (4) |
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Glossopharyngeal nerve neuropathy (cranial nerve IX) |
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|
700 | (2) |
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Selected conditions affecting the glossopharyngeal nerve |
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|
702 | (1) |
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Vagus nerve neuropathy (cranial nerve X) |
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|
703 | (2) |
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Spinal accessory nerve neuropathy (cranial nerve XI) |
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|
705 | (1) |
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Hypoglossal nerve neuropathy (cranial nerve XII) |
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|
706 | (3) |
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Chapter 18 Cranial neuropathies II, III, IV, and VI |
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|
709 | (30) |
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Optic nerve neuropathy (cranial nerve II) |
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|
709 | (14) |
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Cranial nerve III, IV, and VI palsies |
|
|
723 | (16) |
|
Chapter 19 Spinal cord disease |
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|
739 | (38) |
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Introduction to myelopathy |
|
|
739 | (2) |
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Extramedullary spinal cord lesions (extrinsic myelopathy) |
|
|
741 | (3) |
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Intramedullary spinal cord lesions (intrinsic myelopathy) |
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|
744 | (33) |
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Inflammatory myelopathy (e.g. myelitis) |
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|
744 | (2) |
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|
746 | (4) |
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Metabolic and toxic myelopathies |
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|
750 | (1) |
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751 | (4) |
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|
755 | (1) |
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756 | (5) |
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|
761 | (3) |
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Myelopathy associated with motor neuron disease |
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|
764 | (13) |
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Chapter 20 Autonomic nervous system disorders |
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|
777 | (10) |
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|
777 | (10) |
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Chapter 21 Diseases of the peripheral nerve and mononeuropathies |
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|
787 | (68) |
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|
787 | (39) |
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793 | (3) |
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|
796 | (5) |
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Nutrition-related neuropathy |
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|
801 | (2) |
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Neuropathy in systemic disease |
|
|
803 | (1) |
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Guillain-Barre syndrome (GBS)/Acute inflammatory demyelinating polyradiculoneuropathy (AIDP) |
|
|
804 | (3) |
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Chronic acquired demyelinating polyneuropathy |
|
|
807 | (4) |
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|
811 | (4) |
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Immune-mediated brachial plexus neuropathy (IBPN) |
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|
815 | (1) |
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|
816 | (4) |
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Hereditary motor and sensory neuropathy (Charcot--Marie--Tooth disease) |
|
|
820 | (4) |
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Syndromic hereditary peripheral neuropathies |
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|
824 | (2) |
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|
826 | (29) |
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Upper extremity neuropathy |
|
|
826 | (16) |
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Lower extremity neuropathy |
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|
842 | (13) |
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Chapter 22 Neuromuscular junction disorders |
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|
855 | (18) |
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|
855 | (10) |
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Congenital myasthenic syndromes |
|
|
865 | (2) |
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Lambert--Eaton myasthenic syndrome |
|
|
867 | (2) |
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|
869 | (4) |
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Chapter 23 Muscle disorders |
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|
873 | (44) |
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|
873 | (2) |
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875 | (2) |
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|
877 | (7) |
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Critical illness myopathy |
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|
884 | (2) |
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Endocrine and metabolic myopathies |
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|
886 | (9) |
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|
895 | (16) |
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Muscle channelopathies (disorders of membrane excitability) |
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|
911 | (6) |
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Chapter 24 Sleep disorders |
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|
917 | (48) |
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|
917 | (1) |
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|
917 | (6) |
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Commonly performed sleep tests |
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|
923 | (8) |
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|
931 | (4) |
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Hypersomnias of central origin |
|
|
935 | (6) |
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Sleep-related movement disorders |
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|
941 | (4) |
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Sleep-related breathing disorders |
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|
945 | (6) |
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Circadian rhythm sleep disorders |
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|
951 | (5) |
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|
956 | (5) |
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|
961 | (4) |
Index |
|
965 | |