Contributors |
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xi | |
Foreword |
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xiii | |
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Part 1 Hemophilia A and Hemophilia B |
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1 | (118) |
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Section 1 General Overview |
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3 | (26) |
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Introduction 1 The Hemophilic Ankle: An Update |
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5 | (10) |
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E. Carlos Rodriguez-Merchan |
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Introduction 2 The Hemophilic Knee: An Update |
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15 | (14) |
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E. Carlos Rodriguez-Merchan |
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Section 2 Hemophilia with Inhibitors |
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29 | (22) |
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Introduction Study 1 Inhibitor Patient Requiring High Dose Therapy with rVHa as well as Sequential Therapy with FEIBA |
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31 | (4) |
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Introduction Study 2 Prophylactic Therapy in a Patient with a High Titer Inhibitor |
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35 | (2) |
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Introduction Study 3 Immune Tolerance Induction |
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37 | (4) |
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Introduction Study 4 Monitoring During Immune Tolerance Induction |
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41 | (2) |
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Introduction Study 5 Factor IX Inhibitors |
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43 | (2) |
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Introduction Study 6 Severe Hemophilia B with High Response Inhibitor and Anaphylactic Reaction to Factor IX |
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45 | (4) |
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Introduction Study 7 Inhibitor Patient and Dental Surgery |
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49 | (2) |
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Section 3 Hemophilic Treatment for Procedures |
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51 | (34) |
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Introduction Study 8 Deep Vein Thrombosis Prophylaxis in Patients with Hemophilia A Undergoing Orthopedic Surgery |
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53 | (2) |
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Introduction Study 9 Prostate Surgery and Hemophilia |
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55 | (2) |
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Introduction Study 10 Mild Hemophilia and Intraocular Injections |
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57 | (2) |
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Introduction Study 11 Endoscopy/Colonoscopy and Hemophilia |
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59 | (2) |
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Introduction Study 12 Dialysis and Hemophilia |
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61 | (4) |
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Introduction Study 13 Circumcision |
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65 | (2) |
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Introduction Study 14 Pharmacokinetic Studies for Surgery |
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67 | (4) |
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Introduction Study 15 Compartment Syndrome |
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71 | (4) |
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Introduction Study 16 Successful Eradication of Factor VIII Inhibitor in Patient with Mild Hemophilia A Prior to Hemipelvectomy for Extensive Hemophilic Pseudotumor |
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75 | (4) |
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Introduction Study 17 Coronary Artery Disease and Hemophilia |
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79 | (4) |
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Introduction Study 18 Valve Replacement and Hemophilia |
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83 | (2) |
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Section 4 Treatment for Other Conditions |
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85 | (12) |
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Introduction Study 19 Thyroid Biopsy and Hemophilia |
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87 | (4) |
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Introduction Study 20 Atrial Fibrillation and Bleeding Disorders |
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91 | (2) |
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Introduction Study 21 Chronic Upper Gastrointestinal Bleeding and Hemophilia |
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93 | (2) |
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Introduction Study 22 Hematuria |
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95 | (2) |
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Section 5 Other Issues in Hemophilia Care |
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97 | (8) |
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Introduction Study 23 Reproductive Options for Hemophilia A Carriers |
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99 | (4) |
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Introduction Study 24 Mild Hemophilia A with Discrepant FVIII Activity Levels |
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103 | (2) |
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Section 6 Compound Diagnoses |
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105 | (14) |
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Introduction Study 25 Hemophilia A with Tuberous Sclerosis and CNS Bleed |
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107 | (2) |
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Introduction Study 26 Familial Risk Assessment for Individuals with Hemophilia A and von Willebrand Disease |
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109 | (4) |
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Introduction Study 27 Hemophilia A and Hereditary Hemorrhagic Telangiectasia |
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113 | (6) |
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Part 2 von Willebrand Disease |
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119 | (26) |
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Section 1 Management during Procedures |
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121 | (14) |
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Introduction Study 28 Type 1 von Willebrand Disease and Tonsillectomy |
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123 | (2) |
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Introduction Study 29 von Willebrand Disease and Dental Surgery |
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125 | (4) |
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Introduction Study 30 von Willebrand Disease and Gastrointestinal Surgery |
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129 | (6) |
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Gynecologic and Obstetric Considerations: von Willebrand Disease and Obstetric/Gynecologic Procedures |
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132 | (3) |
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Section 2 Rare Forms of von Willebrand Disease |
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135 | (10) |
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Introduction Study 31 Type 2A von Willebrand Disease and Recurrent Gastrointestinal Bleeding |
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137 | (2) |
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Introduction Study 32 Type 2B von Willebrand Disease and Thoracic Surgery |
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139 | (2) |
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Introduction Study 33 von Willebrand Disease 2N |
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141 | (4) |
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Part 3 Other Bleeding Disorders |
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145 | (24) |
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Introduction Study 34 Prothrombin Deficiency |
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147 | (2) |
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Introduction Study 35 Factor V Deficiency |
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149 | (2) |
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Introduction Study 36 Factor VII Deficiency |
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151 | (2) |
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Introduction Study 37 Factor X Deficiency |
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153 | (2) |
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Introduction Study 38 Factor XI Deficiency |
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155 | (2) |
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Introduction Study 39 Factor XIII Deficiency |
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157 | (2) |
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Introduction Study 40 Combined Factor V and Factor VIII Deficiency |
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159 | (4) |
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Introduction Study 41 Glanzmann Thrombaesthenia |
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163 | (2) |
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Introduction Study 42 Gardner-Diamond Syndrome and von Willebrand Disease |
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165 | (2) |
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Introduction Study 43 Qualitative Platelet Disorder |
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167 | (2) |
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Part 4 Acquired Bleeding Disorders |
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169 | (28) |
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Introduction Study 44 Acquired FVIII Inhibitor and B Cell Neoplasm |
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171 | (2) |
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Introduction Study 45 FVIII Inhibitor and Lupus Inhibitor |
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173 | (2) |
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Introduction Study 46 Acquired von Willebrand Disease |
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175 | (6) |
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Introduction Study 47 A Woman with Bleeding Gums |
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181 | (2) |
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Introduction Study 48 Bleeding after Cardiac Surgery |
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183 | (4) |
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Introduction Study 49 Bleeding in a Dialysis Patient |
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187 | (2) |
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Introduction Study 50 A Woman with Anemia and Hematuria |
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189 | (2) |
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Introduction Study 51 Scalp Bleeding in an Older Gentleman |
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191 | (2) |
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Introduction Study 52 Hyperfibrinolysis |
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193 | (4) |
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Part 5 Thrombotic Disorders |
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197 | (22) |
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Introduction Study 53 Heparin-Induced Thrombocytopenia with Thrombosis |
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199 | (4) |
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Introduction Study 54 Heparin Skin Necrosis |
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203 | (2) |
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Introduction Study 55 Warfarin Skin Necrosis |
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205 | (2) |
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Introduction Study 56 Thoracic Outlet Syndrome |
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207 | (2) |
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Introduction Study 57 Antithrombin Deficiency |
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209 | (2) |
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Introduction Study 58 May-Thurner Syndrome |
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211 | (4) |
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Introduction Study 59 Thrombosis in a Liver Transplant Patient |
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215 | (2) |
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Introduction Study 60 Combined Thrombophilia |
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217 | (2) |
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Index |
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219 | |